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báo cáo khoa học: "Congenital spinal tumor in a patient with encephalocele and hydrocephalus: a case report"

Tuyển tập báo cáo các nghiên cứu khoa học quốc tế ngành y học dành cho các bạn tham khảo đề tài: Congenital spinal tumor in a patient with encephalocele and hydrocephalus: a case report | Radmanesh et al. Journal of Medical Case Reports 2011 5 9 http www.jmedicalcasereports.eom content 5 1 9 JOURNALOF medical Ur Case REPORTS CASE REPORT Open Access Congenital spinal tumor in a patient with encephalocele and hydrocephalus a case report Farid Radmanesh1 Farideh Nejat1 Fatemeh Mahjoub2 Mostafa El Khashab3 Abstract Introduction Encephalocele is a rare congenital abnormality of the central nervous system where brain tissue protrudes from a defect in the skull. Some anomalies are associated with encephalocele. However the association of spinal teratoma and encephalocele has not been reported in the English literature. Case presentation We report the case of an Iranian girl with a history of encephalocele surgery who at the age of four years developed an intramedullary spinal teratoma and discuss the pathogenesis of this association. Conclusion To the best of our knowledge this is the first report of an association between encephalocele and spinal teratoma. Introduction Encephalocele refers to a group of rare congenital anomalies of the central nervous system CNS where brain tissue protrudes from a defect in the skull 1 . Its prevalence has been estimated to be 0.8 to four in every 10 000 live births 2 . Teratomas are tumors derived from all three germ layers 3 . In children teratomas are more commonly found in the sacrococcygeal region than in the spinal cord 4 which occurs in one of 38 500 viable births. Intramedullary spinal teratomas are rare tumors 5 . In 41.7 of teratomas a concomitant anomaly of the vertebral canal is found most commonly a diastematomye-lia 4 . However to the best of our knowledge there is nor repot of an association with encephalocele in the English literature. We report a case of encephalocele and lumbar intramedullary teratoma and discuss the possible etiology. Case presentation A four-year old Iranian girl was referred to the neurosurgical department with severe back pain and motor regression. She was the second child of .