Tuyển tập báo cáo các nghiên cứu khoa học quốc tế ngành y học dành cho các bạn tham khảo đề tài: Budd-Chiari syndrome in a 25-year-old woman with Behçet’s disease: a case report and review of the literature | Carvalho et al. Journal of Medical Case Reports 2011 5 52 http content 5 1 52 JOURNAL OF MEDICAL CASE REPORTS CASE REPORT Open Access Budd-Chiari syndrome in a 25-year-old woman with Behcet s disease a case report and review of the literature 1 1 2 2 Daniela T Carvalho Fernando T Oikawa Nilce M Matsuda Paulo RB Evora Alice T Yamada 1 Abstract Introduction The risk that patients with Behpet s disease will develop thrombotic complications has been previously described. Although it is distributed worldwide Behpet s disease is rare in the Americas and Europe. Even though the pathogenic mechanisms of vascular complications of Budd-Chiari syndrome in patients with Behpet s disease are unknown severe vascular complications of Budd-Chiari syndrome associated with Behpet s disease seem to affect mainly young men. Case presentation We report a case of Budd-Chiari syndrome a severe vascular complication that developed in a 25-year-old Afro-Brazilian woman with Behpet s disease. Conclusion Severe vascular complications of Budd-Chiari syndrome in patients with Behpet s disease are much more common in young adult male patients we present a rare case of Budd-Chiari syndrome in a young Afro-Brazilian woman with Behpet s disease. Introduction The risk that young male patients with Behcet s disease will develop thrombotic complications has been previously described 1-3 . Although it has a worldwide distribution Behcet s disease is rare in the Americas and Europe. The purpose of this article is to present an unusual case of Budd-Chiari syndrome in a young Afro-Brazilian woman with Behcet s disease and review the literature of Budd-Chiari syndrome in association with Behcet s disease. Budd-Chiari syndrome is caused by blood clots that completely or partially block the large veins that carry blood from the liver hepatic veins into the inferior vena cava 4 5 . Some people have no overt symptoms but others experience fatigue abdominal pain nausea jaundice
