Tuyển tập báo cáo các nghiên cứu khoa học quốc tế ngành y học dành cho các bạn tham khảo đề tài: Surgical treatment of giant mesenteric fibromatosis presenting as a gastrointestinal stromal tumor: a case report | Stoidis et al. Journal of Medical Case Reports 2010 4 314 http content 4 1 314 jAg JOURNALOF medical ÌỤr case REPORTS CASE REPORT Open Access Surgical treatment of giant mesenteric fibromatosis presenting as a gastrointestinal stromal tumor a case report 1 2 2 3 4 Christos N Stoidis Basileios G Spyropoulos Evangelos P Misiakos Christos K Fountzilas Panorea P Paraskeva Constantine I Fotiadis2 Abstract Introduction Intra-abdominal fibromatosis usually located at the mesenteric level is a locally invasive tumor of fibrous origin with no ability to metastasize but a tendency to recur. Certain non-typical cases of intra-abdominal fibromatosis with involvement of the bowel wall can be misdiagnosed because of their different biological behavior. Case presentation We describe the case of a 64-year-old Caucasian man presenting with mesenteric fibromatosis and involvement of the bowel wall who was treated surgically. The macroscopic and microscopic appearance of the lesion mimicked a gastrointestinal stromal tumor a tumor with potential malignant behavior. Conclusion It is essential to make an early and correct diagnosis in such equivocal cases so that the appropriate treatment can be chosen and suitable patients admitted to clinical trials if appropriate. New and reliable criteria for discriminating between intra-abdominal fibromatosis and gastrointestinal stromal tumor should be proposed and established because novel sophisticated therapeutic strategies have been introduced in the international literature. Introduction Mesenteric desmoids account for less than 10 of sporadic desmoid tumors and are particularly common in patients with familial adenomatous polyposis FAP 1 . Of these tumors 70 are intra-abdominal and most of these involve the mesentery 1 . The association between desmoid tumors and FAP is particularly strong in patients with Gardner s syndrome 2 . Patients with FAP and a family history of desmoid tumors have a 25 chance of .
