Dị dạng đường thở phổi bẩm sinh - CPAM là dị dạng hiếm gặp, tuy nhiên lại là dị dạng hay gặp nhất trong số các dị dạng phổi bẩm sinh. Bệnh có thể được phát hiện từ thời kỳ trước khi sinh đôi khi đến tuổi trưởng thành bệnh mới được phát hiện. Bài viết trình bày đánh giá tỷ lệ và vị trí tổn thương của các tuýp của dị dạng đường thở và phổi bẩm sinh đồng thời tìm hiểu mối liên quan giữa kích thước các nang và tuýp của nó. | Journal of Pediatric Research and Practice Vol. 5 No. 4 2021 3-10 Research Paper Cystic formation and correlation with types of congenital pulmonary airway malformation Nguyen Thi Mai Hoan1 1 Vietnam National Children s Hospital 18 879 La Thanh Dong Da Hanoi Vietnam Received 2 August 2021 Revised 13 August 2021 Accepted 16 August 2021 Abstract Congenital Pulmonary Airway Malformation is a rare disease but the most common form of congenital pulmonary disease. CPAM is a congenital lung disease that can present from the prenatal period to childhood. Though rare overall it is the most common type of congenital lung lesion. Objectives To assess the prevalance and position of the lung lesions of CPAM types furthermore to assess the correlation between size of the cyst and its type. Method A retrospective descriptive study was carried out on all patients admitted to the Respiratory Department of the Vietnam National Children s Hospital with the diagnosis of Congenital Pulmonary Airway Malformation in the period from 2014 to 2019. Results In the period of 6 years there were 79 cases of CPAM admitted to the Respiratory Department. Type I accounted of and type II CPAM accounted for 40 50 32 cases there were 6 cases of type IV accounted for 7 60 . No case of type 0 or type III was found. 4 cases of type II were associated with pulmonary sequestration. In all of the patients the lesions were unilateral mostly found in the lower lobe with the slight prevalence in the right side. Generally type I cyst had large size cysts with the diameter more than were mostly type I. Conclusion CPAM type I was the most common and had potential for malignant transformation. Type I cyst had large size cysts with the diameter more than were mostly type I. CPAM type II was a rare type of congenital pulmonary airway malformation characterized by a multicystic mass of non-functioning lung tissue consisting of small cysts of less than 2 cm in diameter. Keywords Congenital Pulmonary
