Bình thường điện tâm đồ (ECG) (a) và hai tập phim của nhịp tim nhanh tâm thất (b và c) ở bệnh nhân 1 (một kênh ghi âm). (A) có một trục QRS 135 ms, QRS kéo dài, điện áp thấp, và sóng T đảo ngược dẫn precordial. (B) và (c) tỷ lệ nhịp tim nhanh tâm thất là 160 nhịp mỗi phút | Part 3 Historical Pages 203 Br Hun I 8MfcS21-6 Cardiac abnormalities in familial palmoplantar keratosis X PROTONOTARIOS A TSATSOPOULOU p PATSOURAKOS D ALEXOPOULOS p s SIMITSIS G SCAMPARDON1S From the Department of Cardiology 401 Army General Haipaal A them Greece SUMMARY Cardiac abnormalities were identified in patients with familial palmoplantar keratosis. All of them were descended from families on the Greek island of Naxos. Four families were studied and nine cases of palmoplantar keratosis were identified seven of them showed symptoms and signs of heart disease. Cardiomegaly on chest X ray and electrocardiographic abnormalities were common findings. Three cases had episodes of ventricular tachycardia and a fourth patient died suddenly. All patients with cardiac signs and symptoms showed echocardiographic enlargement of the right ventricle and a right venuicular band in three the left ventricle was also affected. Dionysos sits resting on a rock his leg on the thigh of Ariadne a pose symbolic of sacred marriage. Bronze krater from Derveni 320-300 bc. 204 Part 3 Historical Pages Normal electrocardiogram ECG a and two episodes of ventricular tachycardia b and c in patient 1 single channel recorder . In a there was a QRS axis of 135 ms QRS prolongation low voltage and T-wave inversion in the precordial leads. In both b and c the ventricular tachycardia rate is 160 beats per minute and the QRS axes were 75 ms and 135 ms respectively. From Protonotarios N. et al. 1986 See references of his father Jupiter. The wife of Dionysos was Ariadne the daughter of Minos. Dr. Nikos Protonotarios and colleagues examined the population of the Greek island of Naxos and described the so-called Naxos disease in 1986 Protonotarios et al. 1986 A syndrome of arrhythmogenic right ventricular cardiomyopathy ARVC non-epidermolytic palmoplantar keratoderma and woolly hair. The autosomal recessive ARVC of Naxos disease is similar to autosomal dominant ARVC with respect to age and .