Tuyển tập các báo cáo nghiên cứu về y học được đăng trên tạp chí y học Wertheim cung cấp cho các bạn kiến thức về ngành y đề tài: Pulmonary stenosis development and reduction of pulmonary arterial hypertension in atrioventricular septal defect: a case report. | Journal of Cardiothoracic Surgery BioMed Central Open Access Case report Pulmonary stenosis development and reduction of pulmonary arterial hypertension in atrioventricular septal defect a case report Emeline Barth Hélène Bouvaist Stéphanie Marlière Gérard Ninet and Gérald Vanzetto Address Clinique de cardiologie CHU de Grenoble BP 217 38043 Grenoble cedex 09 France Email Emeline Barth - emelinebarth@ Hélène Bouvaist-HBouvaist@ Stéphanie Marlière - Smarliere@ Gérard Ninet - Gérald Vanzetto - Gvanzetto@ Corresponding author Published 16 September 2009 Received 31 March 2009 Journal of Cardiothoracic Surgery 2009 4 49 doi l749-8090-4-49 Accepted 16 September 2009 This article is available from http content 4 1 49 2009 Barth et al licensee BioMed Central Ltd. This is an Open Access article distributed under the terms of the Creative Commons Attribution License http licenses by which permits unrestricted use distribution and reproduction in any medium provided the original work is properly cited. Abstract_ A 24-year-old patient was admitted for dyspnoea and syncope. He had a previous history of complete atrio-ventricular septal defect and trisomy 21. At the age of 6 months in 1984 cardiac catheterization revealed a quasi-systemic pulmonary arterial hypertension with a bidirectional shunt corresponding to an Eisenmenger syndrome. Corrective cardiac surgery was not performed at this time because surgical risk was considered too high. Until the age of 20 years old he showed few symptoms while under medical treatment. But since 2006 his functional status became worse with an increased dyspnoea syncopes and severe cyanosis. In these conditions haemodynamic parameters have been re-evaluated in 2006 and 2008. They highlighted a late and progressive .