This case study was aimed to report the Ectopia cordis in a lamb. A Nellore Jodipi male lamb was presented at the Veterinary Hospital. Clinical examination revealed tachypnea, tachycardia and the presence of an ectopic heart located in the pectoral region. Surgery was performed but the lamb died. Postmortem revealed an opening in the sternum with the presence of a fibrous pericardium attached by ligaments.